The following report describes an extremely rare case of an odontogenic carcinoma derived from a keratocystic odontogenic tumor in a 20yearold man. Senior registrar, professorial unit, royal national throat, nose and ear hospital, grays inn road, london wci x 8da summary. Considering the rarity of this syndrome, we present a 12yearold boy affected by this syndrome. The presence of multiple odontogenic keratocysts can be associated with the gorlingoltz syndrome. The odontogenic keratocyst okc is a cystic lesion of odontogenic origin. Odontogenic keratocysts are aggressive lesions characterised by a high recurrence risk ratio due to dental lamina residues in mandibular and maxillary regions. There are many types of cysts of the jaws, but what makes the odontogenic keratocyst unusual are its characteristic histopathological and clinical features, including potentially aggressive behaviour, high recurrence rate, and an association with the nevoid basal cell carcinoma syndrome. The most characteristic clinical feature of okc is the high recurrence rate. Nasib chand khabra 1, ish pandhi, kiran dn2, sunil alipuria 1, bhawna gulati, and aastha narula1. It is because of this characteristic that a variety of treatment modalities has been suggested for this cyst. Nasib chand khabra 1, ish pandhi 1, kiran dn 2, sunil alipuria 1, bhawna gulati 1, and aastha narula 1. Keratocystic odontogenic tumor are considered to be benign, even though they are locally aggressive and show high recurrence rates after conservative management.
A case report of odontogenic keratocyst in anterior mandibule. The keratocyst odontogenic tumor has characteristics, with slow development, does not cause metastases and. Radiographically, it may appear unilocular or multilocular, with or without defined borders. Pdf keratocystic odontogenic tumor invading the right. Pdf odontogenic keratocyst okc is a cyst of tooth origin with an aggressive clinical behavior including a high recurrence rate. It is now designated by the world health organization as a keratocystic odontogenic tumour kot. Caucasian patient, male, 18 years old, sought care in outpatient oral and maxillofacial surgery. By continuing to use our website, you are agreeing to our use of cookies. Case report radiological and clinical features of peripheral. Case report open access odontogenic keratocyst in the mandible, surgical treatment and reconstruction. Distinguishing squamous odontogenic tumorlike proliferations sotlps is important in odontogenic cysts to avoid misinterpretation such as a squamous odontogenic tumor, welldifferentiated squamous cell carcinoma, and acanthomatous type of ameloblastoma. A 45yearold female patient showed a welldefined radiolucent lesion between the roots of the left second premolar and left first molar. Odontogenic keratocyst okc is an odontogenic cyst and because of its ability in growth and creation tumoral lesions is placed in odontogenic tumor okt.
Case report marcelo guzmanletelier 1, claudia crisostojara 2, camilo diazricouz 3, miguel penarrochadiago 4, david penarrochaoltra 5 dds, maxillofacial surgeon, associate professor, san sebastian university dental school. In this report, a 35yearold male patient was admitted to our clinic with numbness in the left mandible. Pdf odontogenic keratocyst simulating lateral periodontal. In this paper, we shall present one case report of a keratocyst, which derived from an impacted canine. Case report unusual ct appearance in an odontogenic keratocyst of the mandible. During histopathological examination the mass was determined as a keratocyst. Histologic examination revealed an odontogenic keratocyst with no evidence of mineralization or calcification within the lesion. The patient presented with an exophytic lesion in the retromolar region.
Due to highly recurrent nature of the odontogenic keratocysts, patients followup continues. The purpose of this article was to present a case report of odontogenic keratocyst okc arising in the orbital floor, finding the common thread in rare pathology, and highlighting the aberration in our treatment plan by collating all the wealth of information published in the literature. Pdf odontogenic keratocyst mandible an interesting case. We present a case of a odontogenic cyst which followed trauma and histopathologically proved as odontogenic keratocyst.
Okc received its new title as keratocystic odontogenic tumour kcot by the who 2005 in order to suggest its aggressive and recurrent nature. An expansile lesion in the body of the left mandible had high attenuation 225 hu on nonenhanced ct scans. Keratocystic odontogenic tumor kcot, previously referred to as odontogenic keratocyst, is a relatively rare benign intraosseous neoplasm of odontogenic origin that is histopathologically characterized by the presence of a lining of parakeratinized stratified squamous epithelium. Case report keratocystic odontogenic tumor mimicking lateral periodontal cyst. Odontogenic keratocysts appear distinct from other jaw cysts. The distinction between keratocystic odontogenic tumor and other.
Histologic examination revealed an odontogenic ker. Nevoid basal cell carcinoma syndrome, a rare autosomal dominant disorder, comprises a number of abnormalities such as multiple nevoid basal cell carcinomas, skeletal abnormalities and multiple odontogenic keratocysts. Case presentation odontogenic kertocyst presented by dr. The odontogenic keratocyst is a very well known odontogenic cyst. This study is aimed at reporting 4 cases of these clinicopathological proliferations in order to shed more. Odontogenic keratocyst okc is a common developmental odontogenic cyst affecting the maxillofacial region. Alparslan esen 1, ali kilinc 1, yigit guler 1, melek tassoker 2 and omer gunhan 3 1 department of oral and maxillofacial surgery, university of necmettinerbakan, turkey 2 department of oral and maxillofacial radiology, university of necmettinerbakan, turkey 3 department of. Thus, it has been the subject of much research over the last 40 years.
It has specific histopathologic features and aggressive. It can occur anywhere in the jaw, but commonly seen in the posterior part of the mandible. The okc is distinctive among jaw cysts given its tendency toward recurrence and aggressive clinical. The term odontogenic keratocyst was first described by philipsen in 1956. Unusual ct appearance in an odontogenic keratocyst of the. Odontogenic keratocyst of the angle and ramus of the mandible a case report shaveta garg1, m. Thus, the purpose of this study was to report a case of pigmented okc and discuss the hypotheses for this uncommon manifestation. The high attenuation was considered to be due to highly concentrated protein of thick, viscous keratin in the lumen of the keratocyst. Odontogenic keratocyst and uterus bicornis in nevoid basal cell carcinoma syndrome. Okc received its new title as keratocystic odontogenic tumour.
It was formerly known as odontogenic keratocyst okc. K sunil2, ashwarya trivedi3, neetu singla4 abstract the odontogenic keratocyst okc, first described by phillipsen in 1956, has been reclassified as odontogenic neoplasm and has been renamed as keratocystic odontogenic. In 2005, the world health organization who working group considered odontogenic keratocyst okc to be a tumor and recommended the term kcot. Odontogenic keratocyst okc is a common developmental odontogenic cyst affecting the maxillofacial region that arises from the dental lamina. This study is aimed at reporting 4 cases of these clinicopathological proliferations in order to shed more light on the importance of. Odontogenic keratocyst is a locally aggressive and highly recurrent lesion, which occurs mostly on the posterior mandible with a slightly higher rate in males. We analyzed the etiopathogenetic, clinical, radiographic, and histopathologic aspects of keratocystic odontogenic tumors, particularly in association with dental anomalies of number, with the aim of providing useful information for their correct diagnosis, treatment, and prognosis within a multidisciplinary approach. Keratocystic odontogenic tumour kcot previously known as odontogenic keratocyst was recently classified as a benign lesion characterized by an infi we use cookies to enhance your experience on our website.
Case report open access presentation of a keratocystic. The high attenuation was considered to be due to highly concentrated protein of thick, viscous keratin in the lumen of the. Case report a 35 years male came with complaints of swelling in left side of face following trauma to left side of face 1 month back. This cyst actually arises from the cell rests of dental lamina. The authors report an unusal case of okc of the upper jaw.
Odontogenic keratocyst of the angle and ramus of the. Aug 11, 2009 the odontogenic keratocyst is a very well known odontogenic cyst. A clinicopathological report of four cases of squamous. Case reports squamous cell carcinoma arising from an odontogenic keratocyst. Odontogenic keratocyst simulating lateral periodontal cyst. The aim of this case report is to present a keratocystic odontogenic tumor kcot mimicking lateral periodontal cyst. British journal of oral and maxillofacial surgery 1985 23, 210215 1985 the british association of oral and maxillofacial surgeons odontogenic keratocyst of the maxilla. Odontogenic keratocyst an unusual clinical case presentation. They are unique odontogenic lesions that have the potential to behave aggressively, that can recur and can be associated with nevoid basal cell carcinoma syndrome. Patient details 35 year old female reported to bvp opd with cco swelling in lower right back tooth region since 6 months. Odontogenic keratocyst of mandible a case report with.
Clinically, the kot is manifested by an asymptomatic growth. Features of peripheral keratocystic odontogenic tumor 301 int j clin exp med 2014. Odontogenic keratocyst in the mandible, surgical treatment. Multiple okcs are usually seen in association with nevoid basal cell carcinoma syndrome nbccs but approximately 5% of patients with okc have multiple cysts without concomitant syndromic presentation.
We present the case of a 23yearold man with extensive kcot and impacted third molar in the right maxillary sinus. There are many types of cysts of the jaws, but what makes the odontogenic keratocyst unusual are its characteristic histopathological and clinical features, including potentially aggressive behaviour, high recurrence rate, and an association with the nevoid basal cell carcinoma. In this case report, surgical treatment of the odontogenic keratocyst in the right posterior mandible and reconstruction of the defected site is presented. Odontogenic keratocyst a case presentation purshotam nainani 1, anish gupta, pratibha kavle2, amit mathur3 abstract. Journal of oral and maxillofacial surgery, 64, 308316. We describe a case managed conservatively that, in fact, would have required more aggressive treatment.
The clinical, radiological, and histological features of this tumor and its surgical management are discussed. Radiographically, most okcs are unilocular when presented at the periapex and can be mistaken for radicular or lateral periodontal cyst. Odontogenic keratocysts in nevoid basal cell carcinoma. Feb 20, 20 thus, it has been the subject of much research over the last 40 years.
We analyzed the etiopathogenetic, clinical, radiographic, and histopathologic aspects of keratocystic. A case report of odontogenic keratocyst in anterior. In the present case, surgical treatment was performed. Present study is a case report of a 22 year old man presenting with a symptomatic swelling on the gingiva between the mandibular right premolars and canine. Case report the patient, a 14yearold black male was referred for diagnosis of a painless lesion located in the anterior mandibular region. When the cyst is multilocular and located at the molar ramus area, it. A 14yearold caucasian girl presented for observation of bilateral agenesis. Squamous cell carcinoma arising from an odontogenic. The keratocystic odontogenic tumor kcot is a benign uni or multicystic, intraosseous tumor of odontogenic origin 2 that has a slight male predilection and commonly. When the cyst is multilocular and located at the molar ramus area, it may be. Keratocystic odontogenic tumor kcot is a benign intraosseous neoplasm of the jaw. Presentation of a keratocystic odontogenic tumor with. Case report open access presentation of a keratocystic odontogenic tumor with agenesis. Odontogenic keratocyst okc is the cyst arising from the cell rests of dental lamina.
It is thought to originate from dental laminae residues. A case report farnaz falaki 1, zahra delavarian 2, jahanshah salehinejad 3, shadi saghafi 4 1 assistant professor of oral. Fulltext pdf docile splay graft for middle vault reconstruction. In 2005, odontogenic cyst was classified as keratocyst odontogenic tumor due to being aggressive and recurrent. Aggressive osseous commitment result by keratocyst. First described by philipsen in 1956, the odontogenic keratocyst is characterized by a large squamous keratinization of its border, an aggressive growth and a high recurrent rate. Pdf large odontogenic keratocyst of mandible a case report. Okc received its new title as keratocystic odontogenic tumour kcot by the who 2005 in order to. It can occur anywhere in the jaw but is commonly seen in the posterior part of the mandible. Albodbai mh 21 keratocystic odontogenic tumor in the maxillary sinus. Odontogenic keratocyst looks can be deceptive, causing. Involvement of the maxillary sinus is an unusual presentation. Large odontogenic keratocyst of mandible a case report article pdf available in journal of the indian dental association 57.
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